Congenital Lobar Emphysema CLE

An obstructive process which results in progressive expansion of the lobe(s) distal to it. The hyperinflated segment then compresses the surrounding lung tissue. It is most commonly caused by inadequate bronchial cartilage to provide support, but may also result from extrinsic compression. The most commonly affected area is the left upper lobe, then right upper lobe, then right middle lobe. The usual presentation is in a newborn as dyspnea, wheezing, and cough. Workup should not include bronchoscopy as it can cause further air trapping and worsening symptoms. Treatment usually involves lobectomy.

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