Cancer which arises from neural crest cells, which most commonly occur in preschool aged children. Tumor location may be the adrenal glands, neck, pelvis, mediastinum, or any other place where sympathetic ganglion cells are located. It usually presents as an asymptomatic abdominal mass. Workup includes CT and ultrasound, followed by possible BM biopsy and radionuclide scanning. Laboratory evaluation includes blood and urine levels of VMA and HVMA. The most effective treatment is surgical excision.

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