Bullous congenital ichthyosiform erythro-derma; bullous ichthyotic erythroderma;
ichthyosis bullosa of Siemens; ichthyosis hystrix of Curth-Macklin
Congenital ichthyosis with characteristic histologic finding of epidermolytic hyperk-eratosis
Autosomal dominant trait; defect in the genes for keratin 1 and keratin 10
Presents at birth or shortly thereafter as erythema, blistering, and/or scaling; marked hyperkeratosis shortly after birth; scales are small, dark, with corrugated appearance; scales sometimes shedand, reaccumulate; keratotic skin in intertrigi-nous areas which may become macerated and foul smelling; blisters occur in crops, rupturing, and leaving red, painful, denuded base; bullae tend to disappear before age 20; NPS subtype - lacks severe palmoplantar involvement; PS subtype -severe palmoplantar involvement; no ectro-pion
Non-bullous ichthyosiform erythroderma; lamellar ichthyosis; X-linked ichthyosis; epidermolysis bullosa; incontinentia pig-menti; bullous impetigo; staphylococcal scalded skin syndrome
Prednisone; beta carotene; acetretin; tretin-oin; alpha-hydroxy acid
Bale SJ, Compton JG, DiGiovanna JJ (1993) Epi-dermolytic hyperkeratosis. Seminars in Dermatology 12(3):202-209
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Rosacea and Eczema are two skin conditions that are fairly commonly found throughout the world. Each of them is characterized by different features, and can be both discomfiting as well as result in undesirable appearance features. In a nutshell, theyre problems that many would want to deal with.